Henoch-Schonlein purpura
Background
- Usually affects 2-11yr
- 5% of cases are a/w intussusception (abd vasculitis)
- Renal involvement is feared complication
- 95% recover completely
Diagnosis
- Triad:
- Purpuric rash (lower extremity, buttock)
- Acute abdominal pain (Diffuse, colicky)
- Develops after onset of rash
- Arthritis
- Migratory, usually involves knees/ankles
DDx
- Meningococcemia
- Erythema nodosum
- Intussusception
- Rheumatic fever
- Polyarteritis nodosa
- SLE
- RA
- Drug reaction
Work-Up
- UA
- Hematuria, proteinuria
- Chemistry
Treatment
- Supportive
- NSAIDs for pain
Disposition
- Outpt management for most w/ rheum f/u
Source
Rosen's, Tintinalli
